Hyperostosis Frontalis Interna is characterized by the thickening of the frontal bone of the skull. It is not clear that this disorder is actually rare. Some clinicians. Hyperostosis frontalis interna is characterised by benign overgrowth of the inner table of the frontal bone. It is seen most commonly in older females. The etiology . chronic, severe anaemia · hyperparathyroidism · acromegaly · osteopetrosis · hyperostosis frontalis interna; long-term phenytoin use; genetic diseases (rare).

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Affected Populations Hyperostosis Frontalis Interna affects females 9 times more often than males. Hyperostosis frontalis interna HFI. It is part of the triad of Morgagni syndrome. During this hospital stay the presence of grade I obesity, hyperglycemia, hypertriglyceridemia and hyperuricemia was documented. Morgagni-Stewart-Morel syndrome from whonamedit. Loading Stack – 0 images remaining.

[Morgagni-Stewart-Morel syndrome. Case report and review of the literature].

It can cause mental deficiency and loss of hair. The skull thickening may be sessile or nodular, and may affect the bone in a focal or diffuse manner.

Case 2 Case 2. Crouzon Disease is a genetic disorder characterized by abnormalities in the skull, face, and brain caused by premature hiperostosls of the skull. This alteration can occur in isolation or together with neuropsychiatric symptoms, metabolic and endocrine manifestations which together form the Morgagni-Stewart-Morel syndrome. Years Published, Other treatment is symptomatic and supportive.


Case 1 Case 1. Hyperostosis calvariae diffusa and frontsl fronto-parietalis are related entities. About Blog Go ad-free. Read it at Google Books – Find it at Amazon.

The importance of this condition stems mainly from the necessity of not mistaking it for pathology. The skull is made up of several bony plates initially joined by fibrous connective frontla which normally fuse together and harden fronhal a period of several years after growth of the brain. The differential is that of hyperostosis of the skull and includes:. All studies receiving U. Hyperostosis frontalis interna is characterised by benign overgrowth of the inner table of the frontal bone.

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[Morgagni-Stewart-Morel syndrome. Case report and review of the literature].

The risk of transmitting the disorder from affected parent to offspring is 50 percent for each pregnancy regardless of the sex of the resulting child. Human traits, including the classic genetic diseases, are the product of the interaction of two genes, one received from the father and one from the mother.


As a result, scientists feel that this condition may be much more prevalent than suspected, but often goes undetected. Hyperostosis Frontalis Interna has been found in multiple generations suggesting that the disorder may be inherited as a dominant trait. They are not necessary for a differential diagnosis:. Most conspicuously affected are the extremities, jaws, and face. In this regard, the case of a patient who meets criteria for this syndrome is presented and a review of the literature is performed frlntal focus on its pathophysiology.

Many people have no apparent symptoms.

Comparisons may be useful for a differential diagnosis:. Case 4 Case 4. Diabetes Insipidus is due to an abnormality of anti-diuretic hormone vasopresin or ADH originating in the posterior lobe of the pituitary gland. Check for errors and try again. It is hlperostosis known if the disorder is autosomal dominant or X-linked. Torres MA, et al. You can also scroll through stacks with your mouse wheel or the keyboard arrow keys.

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